Table 1

Criteria for diagnosis of ARVD [5]

I. Global and/or Regional Dysfunction and Structural Alterations*
     • Major
     Severe dilatation and reduction of right ventricular ejection fraction with no (or only mild) left ventricular impairment
     Localized right ventricular aneurysms (akinetic or dyskinetic areas with diastolic bulging)
     Severe segmental dilatation of the right ventricle
     • Minor
     Mild global right ventricular dilatation and/or ejection fraction reduction with normal left ventricle
     Mild segmental dilatation of the right ventricle
     Regional right ventricular hypokinesia

II. Tissue Characterization of Wall
     • Major
     Fibrofatty replacement of myocardium on endomyocardial biopsy

III. Repolarisation Abnormalities
     • Minor
     Inverted T waves in right precordial leads (V2 and V3) in people aged >12 years, in absence of right bundle branch block

IV. Depolarization/Conduction Abnormalities
     • Major
     Epsilon waves or localized prolongation (>110 ms) of the QRS complex in right precordial leads (V1 - V3)
     • Minor
     Late potentials (signal-averaged ECG)

V. Arrhythmias
     • Minor
     Left bundle branch block type ventricular tachycardia (sustained and non-sustained) by ECG, Holter or exercise testing
     Frequent ventricular extra-systoles (>1000/24 hours) by Holter

VI. Family History
     • Major
     Familial disease confirmed at necropsy or surgery
     • Minor
     Family history of premature sudden death (<35 years) due to suspected right ventricular dysplasia
     Familial history (clinical diagnosis based on present criteria)

*Detected by echocardiography, angiography, magnetic resonance imaging, or radionuclide scintigraphy.

The diagnosis of ARVD would be fulfilled by the presence of two major, or one major plus two minor criteria or four minor criteria from different groups.

Jain et al. Journal of Cardiovascular Magnetic Resonance 2008 10:32   doi:10.1186/1532-429X-10-32